porphyria en · NOUN
Pronunciation
- /pɔː(ɹ)ˈfɪɹɪə/
Etymology
From porphyrin, from German Porphyrin.
Meanings
-
Any of several usually hereditary abnormalities of porphyrin metabolism characterized by excretion of excess porphyrins in the urine.
However, the appearance of homozygous forms without consanguinity and coincidence of two types of porphyria in the same patient, dual porphyrias, is possible.
2003, M. Lecha, C. Herrero, D. Ozalla, “Porphyrias”, in Andreas D. Katsambas, Torello M. Lotti, editors, European Handbook of Dermatological Treatments, page 419:The term porphyria, derived from the Greek word porphyra, meaning purple, is apt because a hallmark of most of the porphyrias is the overexcretion of porphyrins in urine or feces.
2000, Herbert L. Bonkovsky, Richard W. Lambrecht, “44: Hemochromatosis, iron overload, and porphyria cutanea tarda”, in James C. Barton, Corwin Q. Edwards, editors, Hemochromatosis: Genetics, Pathophysiology, Diagnosis and Treatment, page 453:The usual presenting symptoms and signs of porphyrias are either skin photosensitivity or neurovisceral symptoms and signs.
2010, James C. Barton, Corwin Q. Edwards, Pradyumna D. Phatak, Robert S. Britton, Bruce R. Bacon, Handbook of Iron Overload Disorders, page 160:
Forms
| Spelling | Features | Labels | Source |
|---|---|---|---|
| porphyrias | Number=Plur | lexicographic |
Deriveds
uroporphyria · hematoporphyria · coproporphyria · pseudoporphyria · porphyric
Relateds
Translations (18)
cs porfyrie (abnormality of porphyrin metabolism) · ca porfíria (abnormality of porphyrin metabolism) · ro porfirie (abnormality of porphyrin metabolism) · hu porfíria (abnormality of porphyrin metabolism) · tr porfiria (abnormality of porphyrin metabolism) · pl porfiria (abnormality of porphyrin metabolism) · fi porfyria (abnormality of porphyrin metabolism) · ru порфири́я (abnormality of porphyrin metabolism) · id porfiria (abnormality of porphyrin metabolism) · el πορφυρία (abnormality of porphyrin metabolism) · it porfiria (abnormality of porphyrin metabolism) · hy պորֆիրիա (abnormality of porphyrin metabolism) · et porfüüria (abnormality of porphyrin metabolism) · de Porphyrie (abnormality of porphyrin metabolism) · es porfiria (abnormality of porphyrin metabolism) · sv porfyri (abnormality of porphyrin metabolism) · pt porfiria (abnormality of porphyrin metabolism) · eo porfirio (abnormality of porphyrin metabolism)