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Words, grammatical forms and meanings linked to the ontology.

paroxysmal nocturnal hemoglobinuria en · NOUN

Meanings

  1. (uncountable) A rare, acquired blood disorder in which a mutation in the PIGA gene causes red blood cells to lack protective surface proteins, making them vulnerable to complement-mediated destruction, leading to hemolysis, anemia, dark urine, and increased risk of blood clots.

Forms

SpellingFeaturesLabelsSource
paroxysmal nocturnal haemoglobinuria UK, alternative lexicographic
PNH Abbr=Yes lexicographic

Relateds

paroxysmal cold hemoglobinuria

Synonyms

Marchiafava–Micheli syndrome