en coup de sabre en · ADJ
Pronunciation
- /ɒn ˌkuː də ˈseɪ.bə(ɹ)/ (UK)
- (UK)
Etymology
From French en coup de sabre (literally “by/in a strike of the sword”), so-called because of its resemblance to the scar of a sabre wound.
Meanings
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(not-comparable) Of a subtype of localised scleroderma, having a linear, atrophic depression on the frontoparietal scalp.
Linear scleroderma en coup de sabre is a particular form of linear scleroderma that may not truly be related to the other forms.
2009, Thomas J.A. Lehman, A Clinician's Guide to Rheumatic Diseases in Children, Oxford University Press, →ISBN:The patient is an unusual example of bilateral scleroderma en coup de sabre with distortion of both upper eyelids, and ocular complications.
1962, Harry Maximilian Robinson, Patient presentations of the 12th International Congress of Dermatology:The clinical picture was suggestive of a combination of scleroderma en coup de sabre and facial hemiatrophy (Parry-Romberg syndrome). Distinction between Parry-Romberg syndrome and linear scleroderma with facial atrophy can be quite difficult and it has been postulated that en coup de sabre type may actually be a forme fruste of progressive facial hemiatrophy.
1980, Neurology, India, Neurological Society of India:The en coup de sabre variety probably represents a more superficial form of progressive facial hemiatrophy (the Parry–Romberg syndrome), a condition of slowly progressive atrophy of the soft tissue of half of the face with or without associated dermal sclerosis.
2011, Amy S. Paller, Anthony J. Mancini, Hurwitz Clinical Pediatric Dermatology E-Book: A Textbook of Skin Disorders of Childhood and Adolescence, Elsevier Health Sciences, →ISBN, page 520:Two out of 7 patients with scleroderma en coup de sabre also had morphea elsewhere. These findings strongly favor a close relationship between PFH and scleroderma.
2003, The Journal of Rheumatology: